Chronic Thromboembolic Pulmonary Hypertension
Németh Nóra, Varga Albert
Szegedi Tudományegyetem, Általános Orvostudományi Kar, Családorvosi Intézet
Chronic thromboembolic pulmonary hypertension is a rare complication of pulmonary embolism. The condition is caused by incomplete resolution of the thrombotic material. The fibrotically organised thrombus not only leads to mechanical obstruction in the pulmonary vasculature, but also microvascular remodelling and vasoconstriction occurs. This, in turn, leads to a rise in pulmonary vascular resistance and pulmonary artery pressure. CTEPH markedly harms quality of life and leads to significant mortality. However, this is the only cause of pulmonary hypertension which is curable without lung transplant. Our article summarises steps of diagnostic workup and treatment options for operable and non-operable CTEPH.