Congenital Heart Disease Associated With Pulmonary Hypertension
Bálint Olga Hajnalka, Ablonczy László, Temesvári András
Gottsegen György Országos Kardiológiai Intézet, Budapest
Pulmonary arterial hypertension (PAH) is one of the most severe complication in congenital heart disease. As a consequence of demographic changes in adult congenital population, there is a trend toward less simple shunts and more complex lesions associated to PAH. PAH has prognostic significance, and increases mortality/morbidity in congenital patients. The entire spectrum of PAH specific therapy is available, and it has been shown that is effective in improving the prognosis in these patients.