Treatment of pulmonary hypertension caused by chest wall deformity
█ Case report
Csósza Györgyi1, Valkó Luca2, Baglyas Szabolcs2, Losonczy György1, Lorx András2, Gál János2*, Karlócai Kristóf1*
1Semmelweis Egyetem, Pulmonológia Klinika, Budapest
2Semmelweis Egyetem, Aneszteziológiai és Intenzív Terápiás Klinika, Budapest
*Megosztott utolsó szerzők
Chronic hypoxia associated pulmonary hypertension is most often caused by chronic lung disease but other extrapulmonary factors may also lead to its development. The treatment goal is to diminish hypoxia, which is causal treatment for pulmonary hypertension. In addition to pharmacological treatment of the pulmonary disease, adequate oxygen supplementation is essential, but is not always manageable solely with oxygen therapy. In our case the pulmonary hypertension was the consequence of respiratory failure caused by severe chest deformity and restrictive ventilation disorder. Therefore, long term home non-invasive ventilation with low pressure support and high FiO2 was used to decrease hypoxia; which might reduce progression of pulmonary hypertension in the long haul.